Relationship Between Intracranial Calcifications in Vein of Galen Malformations and Fahr’s Syndrome: A Case Report and Review of the Literature
Journal of Surgery
Volume 4, Issue 2, April 2016, Pages: 13-19
Received: Feb. 3, 2016; Accepted: Feb. 21, 2016; Published: Mar. 19, 2016
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Obande Joseph Orinya, Division of Neurosurgery, Department of Surgery, University of Abuja Teaching Hospital, Gwagwalada-Abuja, Nigeria
Offiong Uduak Mayen, Neurology Unit, Department of Paediatrics, University of Abuja Teaching Hospital, Gwagwalada-Abuja, Nigeria
Jimoh Abdullahi Onimisi, Division of Neurosurgery, Department of Surgery, Ahmadu Bello University Teaching Hospital, Zaria, Nigeria
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Vein of Galen malformations and Fahr’s syndrome are rare neurological disorders. Their neurological manifestations may parallel, as is some radiological presentations in certain scenario. They may be congenital but that may be as far as their similarities go as they are pathologically distinct entities with clearly defined natural courses. The unusual parallel of their characteristic neuroradiological findings in the setting of vein of Galen malformations could becloud diagnosis, due to unfamiliarity with the manifestations as a result of their rarity. Our patient presented post-partial thrombosis of vein of Galen malformation. Neuroimaging showed typical intracranial calcifications of the basal ganglia, subcortical white matter, thalami and cerebellum. The radiological report identified the vein of Galen malformation but also noted that Fahr’s syndrome should be ruled out. The occurrence of intracranial calcifications in the setting of vein of Galen malformation is not a usual event, and normally, in the literatures, vein of Galen malformation is not listed as a cause of multiple intracranial calcifications. Therefore, in such a setting, diagnostic dilemma may occur. We described this patient and reviewed the current literature to clarify mechanism of intracranial calcification formation in vein of Galen malformation.
Calcifications, Vein of Galen, Fahr’s Syndrome, Aneurysm, Neurocognition
To cite this article
Obande Joseph Orinya, Offiong Uduak Mayen, Jimoh Abdullahi Onimisi, Relationship Between Intracranial Calcifications in Vein of Galen Malformations and Fahr’s Syndrome: A Case Report and Review of the Literature, Journal of Surgery. Vol. 4, No. 2, 2016, pp. 13-19. doi: 10.11648/j.js.20160402.12
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This article is an open access article distributed under the Creative Commons Attribution License ( which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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