A Rare Case of Chiari Malformation Type 4
Science Journal of Clinical Medicine
Volume 6, Issue 6, November 2017, Pages: 105-108
Received: Aug. 27, 2017; Accepted: Sep. 27, 2017; Published: Nov. 7, 2017
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Authors
Kelvin Nemayire, Department of Neurosurgery, University of Zimbabwe, Harare, Zimbabwe
Kantenga Dieu merci Kabulo, Department of Neurosurgery, University of Zimbabwe, Harare, Zimbabwe
Nathaniel Zimani, Department of Neurosurgery, University of Zimbabwe, Harare, Zimbabwe
Nyararai Togarepi, Department of Neurosurgery, University of Zimbabwe, Harare, Zimbabwe
Musara Aaron, Department of Neurosurgery, University of Zimbabwe, Harare, Zimbabwe
Kazadi Kaluile Ntenga Kalangu, Department of Neurosurgery, University of Zimbabwe, Harare, Zimbabwe
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Abstract
The Chiari malformations are a family of conditions characterized by developmental or, less commonly, acquired displacements of the cerebellum. The original 19th century description by Hans Chiari delineated 4 types, but only types 1 and 2 are more than just curiosities. In his initial description, Chiari classified the hindbrain malformations into type I, II and III and then latter added type IV malformation. Type IV is a very rare type. It is characterized by cerebellar hypoplasia or aplasia and tentorial hypoplasia. There is no hindbrain herniation in this type. We report a case of a 6 year old male patient who presented to us with a 6 year history of an occipitocervical mass and inability to stand and walk for one year and a 5 month history of headache and vomiting. CT scan of the brain showed a midline posterior fossa bone defect with a meningocele with active obstructive hydrocephalus and hypoplastic cerebellum without hindbrain herniation. A diagnosis of a posterior fossa congenital anomaly (Chiari 4) with obstructive hydrocephalus and occipito-cervical meningocele was made. Ventriculo-peritoneal shunt was inserted three days post admission. Patient was then electively taken to theatre five months later for repair of the occipitocervical meningocele.
Keywords
Chiari Type IV, Hydrocephalus, Meningocele, Hindbrain
To cite this article
Kelvin Nemayire, Kantenga Dieu merci Kabulo, Nathaniel Zimani, Nyararai Togarepi, Musara Aaron, Kazadi Kaluile Ntenga Kalangu, A Rare Case of Chiari Malformation Type 4, Science Journal of Clinical Medicine. Vol. 6, No. 6, 2017, pp. 105-108. doi: 10.11648/j.sjcm.20170606.12
Copyright
Copyright © 2017 Authors retain the copyright of this article.
This article is an open access article distributed under the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0/) which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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