Chiari Network – Just an Innocent Bystander or Can Have Serious Impact on Clinical Outcomes
American Journal of Internal Medicine
Volume 7, Issue 2, March 2019, Pages: 33-35
Received: Mar. 4, 2019;
Accepted: May 14, 2019;
Published: May 30, 2019
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Anum Asif, Department of Medicine, University of Pittsburgh Presbyterian Hospital, Pittsburgh, USA
Nauman Farooq, Department of Medicine, University of Pittsburgh Presbyterian Hospital, Pittsburgh, USA
Tayebah Mumtaz, Department of Medicine, Geisinger Medical Center, Danville, USA
Chiari network, a remnant of sinus venosus is often incidentally diagnosed on routine echocardiograms. Chiari network occurs due to incomplete resorption of right valve of sinus venosus. It is often noticed as fenestrated membranous structure or reticular network like structure in the valve of inferior vena cava and coronary sinus. The structure was first described by Von Rokitansky in 1875 and gained its name after pathologist Hans Chiari in 1897 when he described the structure in 11 cadavers. There are inconsistencies in the exact prevalence of this structure and has been reported in literature from 2-13.6%. Most of this data is available from cadaveric or autopsied hearts. These structures are usually considered as benign congenital malformations but literature has reported various cases which have resulted in medical complications including endocarditis, thromboembolism or procedural difficulties. These structures can also mimic right atrial pathologies or thrombus creating a diagnostic challenge. It is important that clinicians are aware of these since misdiagnosis can have significant effect on clinical course and outcomes of the patients. The possibility of the presence of these congenital remnants should be kept in mind during clinical decision making. We present two clinical scenarios with incidental diagnosis of Chiari network and its effect on the clinical course of these patients.
Chiari Network – Just an Innocent Bystander or Can Have Serious Impact on Clinical Outcomes, American Journal of Internal Medicine.
Vol. 7, No. 2,
2019, pp. 33-35.
Copyright © 2019 Authors retain the copyright of this article.
This article is an open access article distributed under the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0/
) which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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