International Journal of Cardiovascular and Thoracic Surgery

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Extra Anatomic Repair of Interrupted Aortic Arch

Received: 25 September 2019    Accepted: 16 October 2019    Published: 04 November 2019
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Abstract

Interrupted Aortic Arch is a rare congenital anomaly with an incidence of 2 per 100,000 live births. It is almost always (95-97%) associated with structural abnormality like VSD. Interrupted Aortic Arch is usually diagnosed soon after birth, and when left untreated results in 90% mortality at a median age of 4 days. Isolated IAA is a very rare entity. Substantial collateral circulation must be present to maintain flow and enable survival. Conventional surgical repair is a challenge due to extensive collateral circulation in patients who have survived to adulthood. Here, we report a patient with an isolated IAA without any associated defect who survived into third decade. The patient presented with complaints of palpitations, uncontrolled hypertension, and weakness in lower limbs and on evaluation, he had isolated Interrupted Aortic Arch. We managed to do an Extra anatomical Bypass graft from ascending aorta to descending aorta on a beating heart with minimal risk. The procedure was done through median sternotomy to avoid the damage to collaterals when approached through thoracotomy.

DOI 10.11648/j.ijcts.20190505.11
Published in International Journal of Cardiovascular and Thoracic Surgery (Volume 5, Issue 5, September 2019)
Page(s) 72-75
Creative Commons

This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited.

Copyright

Copyright © The Author(s), 2024. Published by Science Publishing Group

Keywords

Interrupted Aortic Arch, Extra Anatomical Bypass, Sternotomy, Collaterals, IAA

References
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Author Information
  • Department of Cardiovascular and Thoracic Surgery, Yashoda Hospitals, Hyderabad, India

  • Department of Cardiovascular and Thoracic Surgery, Yashoda Hospitals, Hyderabad, India

  • Department of Cardiac Anaesthesia, Yashoda Hospitals, Hyderabad, India

  • Department of Cardiovascular and Thoracic Surgery, Yashoda Hospitals, Hyderabad, India

  • Department of Perfusion, Yashoda Hospitals, Hyderabad, India

Cite This Article
  • APA Style

    Anirudh Kumar Paidi, Palli Venkata Naresh Kumar, Madhava Rao Midhe, Ravi Kiran Mamidala, Venkat Reddy Navuluri. (2019). Extra Anatomic Repair of Interrupted Aortic Arch. International Journal of Cardiovascular and Thoracic Surgery, 5(5), 72-75. https://doi.org/10.11648/j.ijcts.20190505.11

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    ACS Style

    Anirudh Kumar Paidi; Palli Venkata Naresh Kumar; Madhava Rao Midhe; Ravi Kiran Mamidala; Venkat Reddy Navuluri. Extra Anatomic Repair of Interrupted Aortic Arch. Int. J. Cardiovasc. Thorac. Surg. 2019, 5(5), 72-75. doi: 10.11648/j.ijcts.20190505.11

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    AMA Style

    Anirudh Kumar Paidi, Palli Venkata Naresh Kumar, Madhava Rao Midhe, Ravi Kiran Mamidala, Venkat Reddy Navuluri. Extra Anatomic Repair of Interrupted Aortic Arch. Int J Cardiovasc Thorac Surg. 2019;5(5):72-75. doi: 10.11648/j.ijcts.20190505.11

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  • @article{10.11648/j.ijcts.20190505.11,
      author = {Anirudh Kumar Paidi and Palli Venkata Naresh Kumar and Madhava Rao Midhe and Ravi Kiran Mamidala and Venkat Reddy Navuluri},
      title = {Extra Anatomic Repair of Interrupted Aortic Arch},
      journal = {International Journal of Cardiovascular and Thoracic Surgery},
      volume = {5},
      number = {5},
      pages = {72-75},
      doi = {10.11648/j.ijcts.20190505.11},
      url = {https://doi.org/10.11648/j.ijcts.20190505.11},
      eprint = {https://download.sciencepg.com/pdf/10.11648.j.ijcts.20190505.11},
      abstract = {Interrupted Aortic Arch is a rare congenital anomaly with an incidence of 2 per 100,000 live births. It is almost always (95-97%) associated with structural abnormality like VSD. Interrupted Aortic Arch is usually diagnosed soon after birth, and when left untreated results in 90% mortality at a median age of 4 days. Isolated IAA is a very rare entity. Substantial collateral circulation must be present to maintain flow and enable survival. Conventional surgical repair is a challenge due to extensive collateral circulation in patients who have survived to adulthood. Here, we report a patient with an isolated IAA without any associated defect who survived into third decade. The patient presented with complaints of palpitations, uncontrolled hypertension, and weakness in lower limbs and on evaluation, he had isolated Interrupted Aortic Arch. We managed to do an Extra anatomical Bypass graft from ascending aorta to descending aorta on a beating heart with minimal risk. The procedure was done through median sternotomy to avoid the damage to collaterals when approached through thoracotomy.},
     year = {2019}
    }
    

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  • TY  - JOUR
    T1  - Extra Anatomic Repair of Interrupted Aortic Arch
    AU  - Anirudh Kumar Paidi
    AU  - Palli Venkata Naresh Kumar
    AU  - Madhava Rao Midhe
    AU  - Ravi Kiran Mamidala
    AU  - Venkat Reddy Navuluri
    Y1  - 2019/11/04
    PY  - 2019
    N1  - https://doi.org/10.11648/j.ijcts.20190505.11
    DO  - 10.11648/j.ijcts.20190505.11
    T2  - International Journal of Cardiovascular and Thoracic Surgery
    JF  - International Journal of Cardiovascular and Thoracic Surgery
    JO  - International Journal of Cardiovascular and Thoracic Surgery
    SP  - 72
    EP  - 75
    PB  - Science Publishing Group
    SN  - 2575-4882
    UR  - https://doi.org/10.11648/j.ijcts.20190505.11
    AB  - Interrupted Aortic Arch is a rare congenital anomaly with an incidence of 2 per 100,000 live births. It is almost always (95-97%) associated with structural abnormality like VSD. Interrupted Aortic Arch is usually diagnosed soon after birth, and when left untreated results in 90% mortality at a median age of 4 days. Isolated IAA is a very rare entity. Substantial collateral circulation must be present to maintain flow and enable survival. Conventional surgical repair is a challenge due to extensive collateral circulation in patients who have survived to adulthood. Here, we report a patient with an isolated IAA without any associated defect who survived into third decade. The patient presented with complaints of palpitations, uncontrolled hypertension, and weakness in lower limbs and on evaluation, he had isolated Interrupted Aortic Arch. We managed to do an Extra anatomical Bypass graft from ascending aorta to descending aorta on a beating heart with minimal risk. The procedure was done through median sternotomy to avoid the damage to collaterals when approached through thoracotomy.
    VL  - 5
    IS  - 5
    ER  - 

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