A Rare Case of Wilsons Disease with Zoophilia

Prakash Barman; Madhurima Khasnobis; Kamal Nath

doi:doi:10.11648/j.ajpn.20190704.11

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A Rare Case of Wilsons Disease with Zoophilia

Prakash Barman, Madhurima Khasnobis, Kamal Nath

Published in American Journal of Psychiatry and Neuroscience (Volume 7, Issue 4)

Received: 19 August 2019 Accepted: 4 October 2019 Published: 17 October 2019

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Abstract

Wilsons Disease also known as hepatolenticular degeneration is a autosomal recessive disorder, characterized by abnormal copper deposition in the liver, brain, and other tissues caused by mutation in the copper transporting gene ATP7B. Patients presents with neurological and hepatic disorder. Psychiatric manifestation are common along with movement disorder but its association with paraphilic disorders like zoophilia is very rare and there is practically no literature regarding this in North-Eatern India. In this article we report the unique case of a 21 year old boy from rural Assam suffering from Wilson’s disease with multiple neuropsychiatric manifestations among which zoophilia was noteworthy. This case report highlights a rare and atypical association between an adolescent patient of Wilson disease & zoophilia--- a relatively rare paraphilic disorder. A 21 year old boy presented in the Psychiatry emergency department in a tertiary care hospital with aggressive, disorganized behavior with reported sexual act with a cow. Examination of the patient also revealed massive organomegaly and K-F ring which on further investigation confirmed the diagnosis of Wilsons Disease. The occurrence of zoophilic behavior in Wilsons disease is very rare and we have not come across any such report regarding this. To conclude, the association between copper deposition in specific brain areas due to Wilsons disease and zoophilic behaviour we need further studies with better investigative modalities, which will in turn help in drawing an individualise treatment plan.

Published in	American Journal of Psychiatry and Neuroscience (Volume 7, Issue 4)
DOI	10.11648/j.ajpn.20190704.11
Page(s)	78-82
Creative Commons	This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited.
Copyright	Copyright © The Author(s), 2024. Published by Science Publishing Group

Keywords

Wilsons Disease, Hepatolenticular Degeneration, Copper Deposition, Adolescent, Neuropsychiatric, Zoophilia

References

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[9]	Scheinberg IH and Sternlieb I. Wilson’s disease. Philadelphia: WB Saunders, 1984.
[10]	Carta MG, Sorbello O, Moro MF, Bhat KM, Demelia E, Serra A, Mura G, Sancassiani F, Piga M, Demelia L. Bipolar disorders and Wilson’s disease. BMC psychiatry. 2012 Dec; 12 (1): 52.
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[19]	Portala K, Westermark K, von Knorring L, et al. Psychopathology in treated Wilson’s disease determined by means of CPRS expert and selfratings. Acta Psychiatr Scand 2000; 101: 104–109.
[20]	Sadock BJ, Sadock VA. Human Sexuality. In Kaplan and Sadock’s Synopsis of Psychiatry, 8th ed. Philadelphia: Lippincott Williams and Wilkins, 2003: 718-728.
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APA Style

Prakash Barman, Madhurima Khasnobis, Kamal Nath. (2019). A Rare Case of Wilsons Disease with Zoophilia. American Journal of Psychiatry and Neuroscience, 7(4), 78-82. https://doi.org/10.11648/j.ajpn.20190704.11

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ACS Style

Prakash Barman; Madhurima Khasnobis; Kamal Nath. A Rare Case of Wilsons Disease with Zoophilia. Am. J. Psychiatry Neurosci. 2019, 7(4), 78-82. doi: 10.11648/j.ajpn.20190704.11

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AMA Style

Prakash Barman, Madhurima Khasnobis, Kamal Nath. A Rare Case of Wilsons Disease with Zoophilia. Am J Psychiatry Neurosci. 2019;7(4):78-82. doi: 10.11648/j.ajpn.20190704.11

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@article{10.11648/j.ajpn.20190704.11,
  author = {Prakash Barman and Madhurima Khasnobis and Kamal Nath},
  title = {A Rare Case of Wilsons Disease with Zoophilia},
  journal = {American Journal of Psychiatry and Neuroscience},
  volume = {7},
  number = {4},
  pages = {78-82},
  doi = {10.11648/j.ajpn.20190704.11},
  url = {https://doi.org/10.11648/j.ajpn.20190704.11},
  eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ajpn.20190704.11},
  abstract = {Wilsons Disease also known as hepatolenticular degeneration is a autosomal recessive disorder, characterized by abnormal copper deposition in the liver, brain, and other tissues caused by mutation in the copper transporting gene ATP7B. Patients presents with neurological and hepatic disorder. Psychiatric manifestation are common along with movement disorder but its association with paraphilic disorders like zoophilia is very rare and there is practically no literature regarding this in North-Eatern India. In this article we report the unique case of a 21 year old boy from rural Assam suffering from Wilson’s disease with multiple neuropsychiatric manifestations among which zoophilia was noteworthy. This case report highlights a rare and atypical association between an adolescent patient of Wilson disease & zoophilia--- a relatively rare paraphilic disorder. A 21 year old boy presented in the Psychiatry emergency department in a tertiary care hospital with aggressive, disorganized behavior with reported sexual act with a cow. Examination of the patient also revealed massive organomegaly and K-F ring which on further investigation confirmed the diagnosis of Wilsons Disease. The occurrence of zoophilic behavior in Wilsons disease is very rare and we have not come across any such report regarding this. To conclude, the association between copper deposition in specific brain areas due to Wilsons disease and zoophilic behaviour we need further studies with better investigative modalities, which will in turn help in drawing an individualise treatment plan.},
 year = {2019}
}

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TY  - JOUR
T1  - A Rare Case of Wilsons Disease with Zoophilia
AU  - Prakash Barman
AU  - Madhurima Khasnobis
AU  - Kamal Nath
Y1  - 2019/10/17
PY  - 2019
N1  - https://doi.org/10.11648/j.ajpn.20190704.11
DO  - 10.11648/j.ajpn.20190704.11
T2  - American Journal of Psychiatry and Neuroscience
JF  - American Journal of Psychiatry and Neuroscience
JO  - American Journal of Psychiatry and Neuroscience
SP  - 78
EP  - 82
PB  - Science Publishing Group
SN  - 2330-426X
UR  - https://doi.org/10.11648/j.ajpn.20190704.11
AB  - Wilsons Disease also known as hepatolenticular degeneration is a autosomal recessive disorder, characterized by abnormal copper deposition in the liver, brain, and other tissues caused by mutation in the copper transporting gene ATP7B. Patients presents with neurological and hepatic disorder. Psychiatric manifestation are common along with movement disorder but its association with paraphilic disorders like zoophilia is very rare and there is practically no literature regarding this in North-Eatern India. In this article we report the unique case of a 21 year old boy from rural Assam suffering from Wilson’s disease with multiple neuropsychiatric manifestations among which zoophilia was noteworthy. This case report highlights a rare and atypical association between an adolescent patient of Wilson disease & zoophilia--- a relatively rare paraphilic disorder. A 21 year old boy presented in the Psychiatry emergency department in a tertiary care hospital with aggressive, disorganized behavior with reported sexual act with a cow. Examination of the patient also revealed massive organomegaly and K-F ring which on further investigation confirmed the diagnosis of Wilsons Disease. The occurrence of zoophilic behavior in Wilsons disease is very rare and we have not come across any such report regarding this. To conclude, the association between copper deposition in specific brain areas due to Wilsons disease and zoophilic behaviour we need further studies with better investigative modalities, which will in turn help in drawing an individualise treatment plan.
VL  - 7
IS  - 4
ER  -

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Author Information

Prakash Barman

Department of Psychiatry, Silchar Medical Colege and Hospital, Silchar, India
Madhurima Khasnobis

Department of Psychiatry, Silchar Medical Colege and Hospital, Silchar, India
Kamal Nath

Department of Psychiatry, Fakharuddin Ali Ahmed Medical College and Hospital, Barpeta, India

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Plain Text BibTeX RIS

APA Style

Prakash Barman, Madhurima Khasnobis, Kamal Nath. (2019). A Rare Case of Wilsons Disease with Zoophilia. American Journal of Psychiatry and Neuroscience, 7(4), 78-82. https://doi.org/10.11648/j.ajpn.20190704.11

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ACS Style

Prakash Barman; Madhurima Khasnobis; Kamal Nath. A Rare Case of Wilsons Disease with Zoophilia. Am. J. Psychiatry Neurosci. 2019, 7(4), 78-82. doi: 10.11648/j.ajpn.20190704.11

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AMA Style

Prakash Barman, Madhurima Khasnobis, Kamal Nath. A Rare Case of Wilsons Disease with Zoophilia. Am J Psychiatry Neurosci. 2019;7(4):78-82. doi: 10.11648/j.ajpn.20190704.11

Copy | Download

@article{10.11648/j.ajpn.20190704.11,
  author = {Prakash Barman and Madhurima Khasnobis and Kamal Nath},
  title = {A Rare Case of Wilsons Disease with Zoophilia},
  journal = {American Journal of Psychiatry and Neuroscience},
  volume = {7},
  number = {4},
  pages = {78-82},
  doi = {10.11648/j.ajpn.20190704.11},
  url = {https://doi.org/10.11648/j.ajpn.20190704.11},
  eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ajpn.20190704.11},
  abstract = {Wilsons Disease also known as hepatolenticular degeneration is a autosomal recessive disorder, characterized by abnormal copper deposition in the liver, brain, and other tissues caused by mutation in the copper transporting gene ATP7B. Patients presents with neurological and hepatic disorder. Psychiatric manifestation are common along with movement disorder but its association with paraphilic disorders like zoophilia is very rare and there is practically no literature regarding this in North-Eatern India. In this article we report the unique case of a 21 year old boy from rural Assam suffering from Wilson’s disease with multiple neuropsychiatric manifestations among which zoophilia was noteworthy. This case report highlights a rare and atypical association between an adolescent patient of Wilson disease & zoophilia--- a relatively rare paraphilic disorder. A 21 year old boy presented in the Psychiatry emergency department in a tertiary care hospital with aggressive, disorganized behavior with reported sexual act with a cow. Examination of the patient also revealed massive organomegaly and K-F ring which on further investigation confirmed the diagnosis of Wilsons Disease. The occurrence of zoophilic behavior in Wilsons disease is very rare and we have not come across any such report regarding this. To conclude, the association between copper deposition in specific brain areas due to Wilsons disease and zoophilic behaviour we need further studies with better investigative modalities, which will in turn help in drawing an individualise treatment plan.},
 year = {2019}
}

Copy | Download

TY  - JOUR
T1  - A Rare Case of Wilsons Disease with Zoophilia
AU  - Prakash Barman
AU  - Madhurima Khasnobis
AU  - Kamal Nath
Y1  - 2019/10/17
PY  - 2019
N1  - https://doi.org/10.11648/j.ajpn.20190704.11
DO  - 10.11648/j.ajpn.20190704.11
T2  - American Journal of Psychiatry and Neuroscience
JF  - American Journal of Psychiatry and Neuroscience
JO  - American Journal of Psychiatry and Neuroscience
SP  - 78
EP  - 82
PB  - Science Publishing Group
SN  - 2330-426X
UR  - https://doi.org/10.11648/j.ajpn.20190704.11
AB  - Wilsons Disease also known as hepatolenticular degeneration is a autosomal recessive disorder, characterized by abnormal copper deposition in the liver, brain, and other tissues caused by mutation in the copper transporting gene ATP7B. Patients presents with neurological and hepatic disorder. Psychiatric manifestation are common along with movement disorder but its association with paraphilic disorders like zoophilia is very rare and there is practically no literature regarding this in North-Eatern India. In this article we report the unique case of a 21 year old boy from rural Assam suffering from Wilson’s disease with multiple neuropsychiatric manifestations among which zoophilia was noteworthy. This case report highlights a rare and atypical association between an adolescent patient of Wilson disease & zoophilia--- a relatively rare paraphilic disorder. A 21 year old boy presented in the Psychiatry emergency department in a tertiary care hospital with aggressive, disorganized behavior with reported sexual act with a cow. Examination of the patient also revealed massive organomegaly and K-F ring which on further investigation confirmed the diagnosis of Wilsons Disease. The occurrence of zoophilic behavior in Wilsons disease is very rare and we have not come across any such report regarding this. To conclude, the association between copper deposition in specific brain areas due to Wilsons disease and zoophilic behaviour we need further studies with better investigative modalities, which will in turn help in drawing an individualise treatment plan.
VL  - 7
IS  - 4
ER  -

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